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Huntingtons Disease
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Parkinsonism in HIV-Infected Patients on Highly Active Antiretroviral Therapy
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A 75-Year-Old Woman with Progressive Right-Hand Tremor and Inability to Use Her Right Side
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Fragile X-Associated Tremor/Ataxia Syndrome: An Aging Face of the Fragile X Gene
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Genetic, Clinical, and Radiographic Delineation of Hallervorden-Spatz Syndrome
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Consequences of the Delayed Diagnosis of Ataxia-Telangiectasia
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CT and MR Findings of Neuroacanthocytosis
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Corticobasal Degeneration:Neuropathologic and Clinical Heterogeneity
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Dentatorubral-Pallidoluysian Atrophy:Clin Features Closely Related to Unstable Expansion of Trinucleotide (CAG) Repeat
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Corticodentatonigral Degeneration with Neuronal Achromasia
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Diseases of the Basal Ganglia-Their Relation to Disorders of Movement
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A Case of Ataxia, Seizure, and Choreoathetosis in a 34-year-old Woman
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Clinical Reasoning: A Woman with Rapidly Progressive Apraxia
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Clinicopathologic Conference, Kufs Disease (Autosomal Dominant) Parry Type Neuronal Ceroid Lypofuscinosis
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Progressive Supranuclear Palsy: A Current Review
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Clinicopath Conf, Neuronal Ceroid Lipofuscinosis, Late-Onset Infantile Subtype
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Recessive Ataxia With Ocular Apraxia
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Molecular Basis of the Neurodegenerative Disorders
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A New Variant of Creutzfeldt-Jakob Disease in the UK
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Trinucleotide Repeat Expansion in Neurological Disease
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Molecular Genetics in Neurology
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The Polymerase Chain Reaction:Application to Nervous System Disease
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Hereditary Dentatorubral-Pallidoluysian Atrophy:Clinical and Pathologic Variants in a Family
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Fragile X-Associated Tremor or Ataxia Syndrome in a Patient with Difficulty Walking, Falls, a Tremor, and Erectile Dysfunction
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Sport Associated Dementia
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Clinicopathologic conference, Frontotemporal Lobar Degeneration with tau-positive inclusions consistent with Picks disease
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Stridor in Multiple System Atrophy
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Hereditary Spastic Paraplegia:From Diagnosis to Emerging Therapeutic Approaches
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Atypical Parkinsonian Syndromes: A General Neurologists Perspective
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Clinicopathologic Conference, Primary Progressive Aphasia, Semantic Variant, due to TAR DNA Binding Protein 43 associated Frontotemporal Lobar Degen
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Amyotrophic Lateral Sclerosis
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Dentate Update: Imaging Features of Entities that Affect the Dentate Nucleus
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Neuroimaging Changes in Menkes Disease, Part 1
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Intrathecal 2-hydroxypropyl-�-cyclodextrin Decreases Neurological Disease Progression in Niemann-Pick disease, type C1: a non-randomised, open-label, phase 1-2 trial
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Leukodystrophy and Progressive Myoclonic Epilepsy Disclosing DRPLA
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Orthostatic Myoclonus Associated with CASPR2 Antibodies
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A Young Man with Progressive Language Difficulty and Early-Onset Dementia
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Multiple-System Atrophy
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Clinicopathologic Conference, Frontotemporal Lobar Degeneration with Tau-positive Inclusions (Picks Disease Subtype) Due to a Gly389Arg MAPT Mutation, Resulting in the Behavioral Variant of Frontotemporal Dementia with Parkinsonism
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Treatment of Multiple System Atrophy Using Intravenous Immunoglobulin
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Differential Diagnosis of Bilateral Abnormalities of the Basal Ganglia and Thalamus
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Skin biopsy is useful for the antemortem diagnosis of neuronal intranuclear inclusion disease
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Rapidly Progressive Neurodegenerative Dementias
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Spinal Muscular Atrophy
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Rapidly Progressive Dementia
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